Un Skull base dermoid cyst fistulizing to the nasal tip in a pediatric patient: case report

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Martín Pinzón
Catalina Jaramillo-Moncayo
Manuela Orozco-Naranjo

Abstract

The dermoid cyst is a rare congenital lesion, secondary to an incomplete regression of ectodermal tissue. It’s incidence is 1/20,000-40,000 live births. Timely surgical resection must be performed to prevent intracranial involvement and/or complications. Imaging study determines it’s extension. Different surgical approaches have been recommended, all must adhere to Pollock’s 4 principles. The following study presents the case of a pediatric patient, 9 months old, with a dermoid cyst at the skull base with a fistulous path to the nasal tip. Contrasted nuclear magnetic resonance revealed a cystic mass in the region anterior to the crista galli communicated with a fistulous tract at the nasal tip. The patient was taken to surgery for cyst resection by external rhinoplasty combined with a transnasal endoscopic approach with satisfactory functional and aesthetic results, without recurrence. A Cerebrospinal fluid fistula was evidenced, as an intraoperative complication, it was corrected in the same surgical time.

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How to Cite
1.
Pinzón M, Jaramillo-Moncayo C, Orozco-Naranjo M. Un Skull base dermoid cyst fistulizing to the nasal tip in a pediatric patient: case report. Acta otorrinolaringol cir cabeza cuello [Internet]. 2022Jan.31 [cited 2024Jul.3];49(4):304 -309. Available from: https://revista.acorl.org.co/index.php/acorl/article/view/555
Section
Reportes de Casos
Author Biography

Catalina Jaramillo-Moncayo, Fundación Universitaria Ciencias de La Salud

Médica egresada de La Universidad de Los Andes, Bogotá - Colombia. 

Residente del programa de Otorrinolaringología de La Fundación Universitaria Ciencias de La Salud, Hospital de San José. Bogotá - Colombia.

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